Hearing Loss and Mitochondrial Disease

Do you have hearing loss that is sensorineural that affects the inner ear and neural loss involving the hearing nerve? (vestibulocochlear nerve)

Sensorineural hearing loss is a type of hearing loss, or deafness, in which the root cause lies in the inner ear or sensory organ or the vestibulocochlear nerve.

Is your hearing loss intermittent and affects one or both ears?

Did your hearing loss begin at a young age?

Do you have one or more family members that also experience hearing loss?

Has your hearing loss been described by doctors as “atypical”?

Your hearing loss may be associated with mitochondrial disease (mito).

Mito is caused by a fault in one or more of our genes. These faulty genes can be inherited from the mother or the father. Recent research demonstrates that mitochondrial mutations are present in at least 1 in 200 people and that around 1 in 5,000 will develop serious illness.

Sensorineural hearing loss is the most common type of permanent hearing loss and the main cause of hearing impairment of those affected with mito. Two-thirds of mito patients experience hearing loss, from very mild to profound deafness. Hearing loss can be the sole symptom of mito or can be one of many other symptoms.

The most common accompanying symptoms of mito are fatigue, muscle weakness, neurological symptoms, digestive issues and weakness in the eyes.

Looking for more information on hearing loss in Mitochondrial Disease?

Contact a mito support officer

RECOGNISING MITO

What are the symptoms of mito?

Mito can be summarised as…

any symptom, in any organ, at any age.

The diagram below shows the organ systems that may be affected and the wide range of different symptoms that can be associated with mito.

Maybe It's Mito Diagram

Looking for more information on hearing loss in Mitochondrial Disease?

Contact a mito support officer

** Red flag symptoms can include diabetes, seizures and ‘salt and pepper’ retinopathy.